Preferred term
- Created
- 1986-08-28T00:00:00Z
- void:inDataset
- http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc
- Notation
- 16735
gangliosidosis
Definition
A complete explanation of the intended meaning of a concept- La gangliosidose généralisée est une maladie des mammifères qui se transmet de manière autosomique récessive.
- Las gangliosidosis son un conjunto de enfermedades de almacenamiento lisosómico hereditarias debidas a un acúmulo de gangliósidos (un tipo de esfingolípidos), sobre todo en las neuronas
- The gangliosidoses are a group of inherited metabolic diseases caused by a deficiency of the different proteins needed to break down lipids.
Broader concept
Broader conceptIn other languages
Terms for the concept in other languages.French
-
gangliosidose
- Created
- 1998-08-04T00:00:00Z
- Last modified
- 2021-06-16T21:24:42Z
- void:inDataset
- http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc
- Notation
- 16735
Portuguese
-
gangliosidose
- Created
- 1998-08-04T00:00:00Z
- Last modified
- 2021-06-16T21:24:42Z
- void:inDataset
- http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc
- Notation
- 16735
Spanish
-
Gangliosidosis
- Created
- 1990-06-18T00:00:00Z
- void:inDataset
- http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc
- Notation
- 16735
URI
http://aims.fao.org/aos/agrovoc/c_16735